4.5 Article

Expression of wild-type human superoxide dismutase-1 in mice causes amyotrophic lateral sclerosis

Related references

Note: Only part of the references are listed.
Article Biochemistry & Molecular Biology

Mutant superoxide dismutase-1 indistinguishable from wild-type causes ALS

Matthis Synofzik et al.

HUMAN MOLECULAR GENETICS (2012)

Article Multidisciplinary Sciences

Axonal transport deficits and degeneration can evolve independently in mouse models of amyotrophic lateral sclerosis

Petar Marinkovic et al.

PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2012)

Article Biotechnology & Applied Microbiology

Astrocytes from familial and sporadic ALS patients are toxic to motor neurons

Amanda M. Haidet-Phillips et al.

NATURE BIOTECHNOLOGY (2011)

Review Clinical Neurology

Clinical genetics of amyotrophic lateral sclerosis: what do we really know?

Peter M. Andersen et al.

NATURE REVIEWS NEUROLOGY (2011)

Review Clinical Neurology

Molecular pathways of motor neuron injury in amyotrophic lateral sclerosis

Laura Ferraiuolo et al.

NATURE REVIEWS NEUROLOGY (2011)

Article Multidisciplinary Sciences

Intermolecular transmission of superoxide dismutase 1 misfolding in living cells

Leslie I. Grad et al.

PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2011)

Article Clinical Neurology

Multiple system degeneration with basophilic inclusions in Japanese ALS patients with FUS mutation

Takahisa Tateishi et al.

ACTA NEUROPATHOLOGICA (2010)

Article Biochemistry & Molecular Biology

An examination of wild-type SOD1 in modulating the toxicity and aggregation of ALS-associated mutant SOD1

Mercedes Prudencio et al.

HUMAN MOLECULAR GENETICS (2010)

Article Biochemistry & Molecular Biology

Superoxide dismutase-1 and other proteins in inclusions from transgenic amyotrophic lateral sclerosis model mice

Daniel Bergemalm et al.

JOURNAL OF NEUROCHEMISTRY (2010)

Article Multidisciplinary Sciences

Novel Antibodies Reveal Inclusions Containing Non-Native SOD1 in Sporadic ALS Patients

Karin Forsberg et al.

PLOS ONE (2010)

Article Multidisciplinary Sciences

Role of mutant SOD1 disulfide oxidation and aggregation in the pathogenesis of familial ALS

Celeste M. Karch et al.

PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2009)

Article Biochemistry & Molecular Biology

Biological effects of CCS in the absence of SOD1 enzyme activation: implications for disease in a mouse model for ALS

Jody B. Proescher et al.

HUMAN MOLECULAR GENETICS (2008)

Article Multidisciplinary Sciences

Initiation and elongation in fibrillation of ALS-linked superoxide dismutase

Madhuri Chattopadhyay et al.

PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2008)

Article Multidisciplinary Sciences

Soluble misfolded subfractions of mutant superoxide dismutase-1s are enriched in spinal cords throughout life in murine ALS models

Per Zetterstrom et al.

PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2007)

Article Multidisciplinary Sciences

Overexpression of CCS in G93A-SOD1 mice leads to accelerated neurological deficits with severe mitochondrial pathology

Marjatta Son et al.

PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2007)

Article Clinical Neurology

Motor neuron disease in mice expressing the wild type-like D90A mutant superoxide dismutase-1

P. Andreas Jonsson et al.

JOURNAL OF NEUROPATHOLOGY AND EXPERIMENTAL NEUROLOGY (2006)

Article Multidisciplinary Sciences

Conversion to the amyotrophic lateral sclerosis phenotype is associated with intermolecular linked insoluble aggregates of SOD1 in mitochondria

HX Deng et al.

PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2006)

Article Multidisciplinary Sciences

Systematically perturbed folding patterns of amyotrophic lateral sclerosis (ALS)-associated SOD1 mutants

MJ Lindberg et al.

PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2005)

Review Biochemistry & Molecular Biology

Neurodegenerative diseases: a decade of discoveries paves the way for therapeutic breakthroughs

MS Forman et al.

NATURE MEDICINE (2004)

Article Multidisciplinary Sciences

Common denominator of Cu/Zn superoxide dismutase mutants associated with amyotrophic lateral sclerosis: Decreased stability of the apo state

MJ Lindberg et al.

PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA (2002)